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Intake and blood levels of fatty acids in treated patients with phenylketonuria



Intake and blood levels of fatty acids in treated patients with phenylketonuria



Journal of Pediatric Gastroenterology and Nutrition 33(3): 253-259



Background: Investigators in Italy and Spain have suggested that therapy for patients with phenylketonuria (PKU) may result in essential fatty acid (EFA) deficiency. Objectives of this study were to determine if the diets of patients with PKU in USA provided adequate EFA intakes and whether patients could form long-chain polyunsaturated fatty acids.

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Accession: 003480100

Download citation: RISBibTeXText

PMID: 11593118

DOI: 10.1097/00005176-200109000-00005


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