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Development of carcinoma carcinoma of the vulva in netherton's syndrome congenital ichthyosiform erythroderma atopic dermatitis trichorrhexis nodosa

Development of carcinoma carcinoma of the vulva in netherton's syndrome congenital ichthyosiform erythroderma atopic dermatitis trichorrhexis nodosa

Geburtshilfe und Frauenheilkunde 47(10): 742-744

So far there has been only one incidence of a malignant tumor associated with Netherton's syndrome, a rare skin disease consisting of congenital ichthyosiform erythroderma, atopic dermatitis and trichorrhexis nodosa (bamboo hair). The aetiology and clinical consequences are discussed on the occasion of a carcinoma of the vulva occurring in a case of a patient with Netherton's syndrome, both phenomena being interlinked.

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Accession: 005132847

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