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Lack of kino cilia in the nasal mucosa in the immotile cilia syndrome



Lack of kino cilia in the nasal mucosa in the immotile cilia syndrome



European Journal of Respiratory Diseases 63(6): 558-563



Ultrastrucutral alterations are described as observed in the nasal mucosa from 2 girl siblings, aged 11 and 14 yr, who had chronic bronchitis, bronchiectasis, recurrent pneumonia and unexplained history of sinusitis and recurrent otitis media since early infancy. Both patients showed, instead of normal ciliated cells, abnormal cells showing on their free surface cilium-like projections without an internal axonemal structure. These abnormal cells, lacking basal bodies, centrioles and kinocilia, presented the same pattern of subcellular components as that occurring in the normal ciliated cells. The possibility that these cells represent a result of genetic mutation is discussed.

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Accession: 005790043

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PMID: 7173350


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