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The operative treatment of epidermolysis bullosa hereditaria

Zeitschrift für Kinderchirurgie 33(2): 175-181

The operative treatment of epidermolysis bullosa hereditaria

After demonstrating four clinical patterns of epidermolysis bullosa hereditaria the operative procedure will be discussed in two cases. One is a now 16-year-old male, the other a 18-year-old girl, who suffer from this disease. While removing the affected skin in a first operation, the defect is covered by a split skin graft taken from a non-affected area. In a second operation or in repeated operative procedures, not only must the affected skin be removed but also any existing scars and contractures. Children who suffer from this form of epidermolysis bullosa hereditaria present a severe problem. For all who deal with this problem, the painstaking preoperative preparation as well as the choice of the most suitable anaesthetic are as important in every respect as the operation itself and the postoperative and psychosocial care.

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Accession: 006728432

PMID: 7282084

Related references

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