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Remission of severe epidermolysis bullosa acquisita induced by extracorporeal photochemotherapy



Remission of severe epidermolysis bullosa acquisita induced by extracorporeal photochemotherapy



British Journal of Dermatology 133(3): 467-471



We report a patient with severe epidermolysis bullosa acquisita (EBA) whose disease was refractory to conventional treatments. New bullae continued to develop over greater than 50% of his body surface area despite therapy. His course was complicated by hyperglycaemia, sepsis, hypoxia caused by pulmonary Aspergillus infection and an idiopathic cardiomyopathy. His EBA resolved after treatment with extracorporeal photochemotherapy (ECP). Hence, ECP may be effective in the treatment of severe EBA which has failed to respond to standard treatment regimens.

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Accession: 009335338

Download citation: RISBibTeXText

PMID: 8547007

DOI: 10.1111/j.1365-2133.1995.tb02680.x



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