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Urticarial pathology in Schnitzler's (hyper-IgM) syndrome



Urticarial pathology in Schnitzler's (hyper-IgM) syndrome



Dermatology 193(2): 94-99



Background: Schnitzler's syndrome is a rare disorder characterized by chronic urticaria and monoclonal IgM gammopathy. The mechanisms of the urticarial flares remain poorly understood. Objective: To more accurately define the histopathologic changes in urticarial lesions, we reviewed 25 original biopsies from 15 cases of Schnitzlei's syndrome, 11 of which have previously been reported. Results: Thirteen specimens from 9 patients showed urticaria with neutrophils (neutrophilic urticaria).

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Accession: 009702127

Download citation: RISBibTeXText

PMID: 8884142

DOI: 10.1159/000246220


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