Medium chain acyl coenzyme a dehydrogenase deficiency apparent michaelis constant and maximal velocity values for fibroblast acyl coenzyme a dehydrogenase towards octanoyl coenzyme a in patient and control cell lines
Gregersen, N.; Kolvraa, S.
Journal of Inherited Metabolic Disease 7(Suppl 2): 105-106
1984
ISSN/ISBN: 0141-8955 Accession: 028691098
PDF emailed within 1 workday: $29.90
Related References
Gregersen, N.; Klvraa, S. 1984: Medium chain acyl-CoA dehydrogenase deficiency: apparent Km and Vmax values for fibroblast acyl-CaO dehydrogenase towards octanoyl CoA in patient and control cell lines Journal of Inherited Metabolic Disease 7(2): 105-106Gregersen, N.; Kølvraa, S. 1984: Medium chain acyl-CoA dehydrogenase deficiency: apparent Km and Vmax values for fibroblast acyl-CoA dehydrogenase towards octanoyl CoA in patient and control cell lines Journal of Inherited Metabolic Disease 7(Suppl 2): 105-106
D.D.nato S.; Gellera, C. 1990: Short chain and medium chain acyl coenzyme a dehydrogenase are lowered in riboflavin responsive lipid myopathies with multiple acyl coenzyme a dehydrogenase deficiency Tanaka, K And P M Coates (Ed ) Progress in Clinical And Biological Research, Vol 321 Fatty Acid Oxidation: Clinical, Biochemical, And Molecular Aspects; International Symposium, Philadelphia, Pennsylvania, Usa, November 6-9, 1988 Xxii+728p Alan R Liss, Inc : New York, New York, Usa Illus 325-332
Ikeda, Y.; Keese, S.M.; Coates, P.M.; Tanaka, K. 1985: Molecular study of mutant medium chain acyl coenzyme a dehydrogenase in cultured fibroblasts from patients with medium chain acyl coenzyme a dehydrogenase deficiency Pediatric Research 19(4 Part 2): 249A
Naito, E.; Indo, Y.; Tanaka, K. 1990: Identification of two variant short chain acyl-coenzyme a dehydrogenase alleles, each containing a different point mutation in a patient with short chain acyl-coenzyme a dehydrogenase deficiency Journal of Clinical Investigation 85(5): 1575-1582
Matsubara, Y.; Indo, Y.; Naito, E.; Ozasa, H.; Glassberg, R.; Vockley, J.; Ikeda, Y.; Kraus, J.; Tanaka, K. 1989: Molecular cloning and nucleotide sequence of cDNAs encoding the precursors of rat long chain acyl-coenzyme A, short chain acyl-coenzyme A, and isovaleryl-coenzyme a dehydrogenases. Sequence homology of four enzymes of the acyl-CoA dehydrogenase family Journal of Biological Chemistry 264(27): 16321-16331
Lau, S.M.; Powell, P.; Buettner, H.; Ghisla, S.; Thorpe, C. 1986: Medium-chain acyl coenzyme a dehydrogenase from pig kidney has intrinsic enoyl coenzyme a hydratase activity Biochemistry 25(15): 4184-4189
Zhou J Z.; Thorpe, C. 1987: Medium chain acyl coenzyme a dehydrogenase from pig kidney inactivation of the reduced enzyme by 2 octynoyl coenzyme a Edmondson, D E And D B Mccormick (Ed ) Flavins And Flavoproteins; Proceedings Of The Ninth International Symposium, Atlanta, Georgia, Usa, June 7-12, Xxiii+775p Walter De Gruyter And Co : Berlin, West Germany; Hawthorne, New York, Usa Illus 173-176
Naito, E.; Ozasa, H.; Ikeda, Y.; Tanaka, K. 1989: Molecular cloning and nucleotide sequence of complementary DNAs encoding human short chain acyl-coenzyme A dehydrogenase and the study of the molecular basis of human short chain acyl-coenzyme A dehydrogenase deficiency Journal of Clinical Investigation 83(5): 1605-1613
Stanley, C.A.; Corkey, B.E.; Booz, G.; Hale, D.E.; Glennon, M.C.; Berry, G.T. 1987: Hepatic acyl coenzyme a profiles in riboflavin deprivation induced multiple acyl coenzyme a dehydrogenase deficiency Pediatric Research 21(4 Part 2): 348A
Hall, C.L. 1982: Effects of concentration and temperature on reduction of electron transfer flavo protein by general acyl coenzyme a dehydrogenase and octanoyl coenzyme a Federation Proceedings 41(4): Abstract 5154
Hall, C.L. 1983: Effects of ferri cyanide upon the reduction of electron transferring flavo protein by general acyl coenzyme a dehydrogenase and octanoyl coenzyme a Federation Proceedings 42(7): Abstract 2086
Naito, E.; Ozasa, H.; Ikeda, Y.; Tanaka, K. 1990: Molecular cloning and nucleotide sequence of complementary dna encoding human short chain acyl coenzyme a dehydrogenase and study of the molecular basis of human short chain acyl coenzyme a dehydrogenase deficiency Tanaka, K And P M Coates (Ed ) Progress in Clinical And Biological Research, Vol 321 Fatty Acid Oxidation: Clinical, Biochemical, And Molecular Aspects; International Symposium, Philadelphia, Pennsylvania, Usa, November 6-9, 1988 Xxii+728p Alan R Liss, Inc : New York, New York, Usa Illus 625-632
Finocchiaro, G.; Tanaka, K. 1986: Purification and characterization of short chain and medium chain acyl coenzyme a dehydrogenases and of isovaleryl coenzyme a dehydrogenase from human liver Federation Proceedings 45(6): 1889
Pellett, J.D.; Sabaj, K.M.; Stephens, A.W.; Bell, A.F.; Wu, J.; Tonge, P.J.; Stankovich, M.T. 2000: Medium-chain acyl-coenzyme a dehydrogenase bound to a product analogue, hexadienoyl-coenzyme A: effects on reduction potential, pK(a), and polarization Biochemistry 39(45): 13982-13992
Powell, P.J.; Thorpe, C. 1988: 2-octynoyl coenzyme a is a mechanism-based inhibitor of pig kidney medium-chain acyl coenzyme a dehydrogenase: isolation of the target peptide Biochemistry 27(21): 8022-8028
Schmidt Sommerfeld, E.; Penn, D.; Kerner, J.; Bieber, L.L. 1990: Acylcarnitines in the urine of a patient with medium chain acyl coenzyme a dehydrogenase mcad deficiency and in normal children Tanaka, K And P M Coates (Ed ) Progress in Clinical And Biological Research, Vol 321 Fatty Acid Oxidation: Clinical, Biochemical, And Molecular Aspects; International Symposium, Philadelphia, Pennsylvania, Usa, November 6-9, 1988 Xxii+728p Alan R Liss, Inc : New York, New York, Usa Illus 403-410
Schmidt Sommerfeld, E.; Penn, D.; Bieber, L.L. 1989: Quantitation of urinary carnitine esters in a patient with medium chain acyl coenzyme a dehydrogenase deficiency mcadd Pediatric Research 25(4 Part 2): 203A
Waber, L.; Francomano, C.; Brusilow, S.; Valle, D.; Frerman, F.; Goodman, S. 1984: Medium chain acyl coenzyme dehydrogenase deficiency Pediatric Research 18(4 Part 2): 302A
Bennett, M.J.; Hale, D.E. 1992: Medium chain acyl-coenzyme a dehydrogenase deficiency New Jersey Medicine: the Journal of the Medical Society of new Jersey 89(9): 675-678