+ Site Statistics
+ Search Articles
+ PDF Full Text Service
How our service works
Request PDF Full Text
+ Follow Us
Follow on Facebook
Follow on Twitter
Follow on LinkedIn
+ Subscribe to Site Feeds
Most Shared
PDF Full Text
+ Translate
+ Recently Requested

Muco lipidosis iv deficiency of ganglioside neuraminidase activity toward sialic acid galactose but not sialic acid sialic acid linkages

Muco lipidosis iv deficiency of ganglioside neuraminidase activity toward sialic acid galactose but not sialic acid sialic acid linkages

Pediatric Research 16(4 Part 2): 189A

Please choose payment method:

(PDF emailed within 1 workday: $29.90)

Accession: 028752597

Download citation: RISBibTeXText

Related references

Muco lipidosis i elevated level of sialic acid containing compounds and deficiency of a neuraminidase in cultured fibroblasts. Human Heredity 27(3): 168, 1977

The metabolic defect in muco lipidosis i accumulation of sialic acid containing compounds due to an alpha neuraminidase ec deficiency. Hoppe-Seyler's Zeitschrift fuer Physiologische Chemie 358(10): 1189, 1977

Amino acid residues important for CMP-sialic acid recognition by the CMP-sialic acid transporter: analysis of the substrate specificity of UDP-galactose/CMP-sialic acid transporter chimeras. Glycobiology 22(12): 1731-1740, 2012

Muco lipidosis part 1 increased sialic acid content and deficiency of an alpha n acetyl neuraminidase in cultured fibroblasts. Biochemical and Biophysical Research Communications 74(2): 732-738, 1977

Incorporation of glycosidically linked sialic acid from radiolabeled free sialic acid and cytidine monophosphate-sialic acid by intact hamster fibroblasts: a reexamination. Biochemistry 19(9): 1893-1900, 1980

Content of gangliosides ano protein bound sialic acid in post mortem brain of patients with muco lipidosis i and muco lipidosis ii. Cellular & Molecular Biology 25(4): 281-284, 1979

Studies on sialic acid. III. Synthesis of sialic acid and a sialic acid-containing substance by Escherichia coli. Fukushima Jour Med Sci 6(1): 61-65, 1958

A highly efficient multienzyme system for the one step synthesis of a sialyl trisaccharide in situ generation of sialic acid and n acetyllactosamine coupled with regeneration of udp glucose udp galactose and cmp sialic acid. Journal of the American Chemical Society 113(16): 6300-6302, 1991

Double labeling on the two faces of the same section with lectin-gold and silver enhancement. Ultrastructural detection of the terminal disaccharides sialic acid-beta-galactose and sialic acid-alpha-N-acetylgalactosamine. European Journal of Histochemistry 41(3): 231-233, 1997

Substrate recognition by UDP-galactose and CMP-sialic acid transporters. Different sets of transmembrane helices are utilized for the specific recognition of UDP-galactose and CMP-sialic acid. Journal of Biological Chemistry 276(24): 21555-21561, 2001

Identification of potential glycan cancer markers with sialic acid attached to sialic acid and up-regulated fucosylated galactose structures in epidermal growth factor receptor secreted from A431 cell line. Molecular and Cellular Proteomics 12(5): 1239-1249, 2013

Plasma sialic acid in animal models of diabetes mellitus: evidence for modulation of sialic acid concentrations by insulin deficiency. Life Sciences 57(14): 1383-1391, 1995

Turnover of free sialic acid, CMP-sialic acid, and bound sialic acid in rat brain. Journal of Neurochemistry 36(4): 1492-1499, 1981

First synthesis of a pentasaccharide moiety of ganglioside GAA-7 containing unusually modified sialic acids through the use of N-Troc-sialic acid derivative as a key unit. Organic Letters 14(24): 6342-6345, 2012

Analysis of sialic acid-related substances and its clinical application. A. Analysis of sialic acid in clinical specimens other than sera. 1. Analysis of total urinary sialic acid, with special reference to the fluctuations in children. Rinsho Byori. Japanese Journal of Clinical Pathology Suppl 54: 165-168, 1983