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Gaucher's disease;thirty-two years experience at Siriraj Hospital
A study of Macrobathra Meyrick from China (Lepidoptera, Cosmopterigidae)
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A revision of world Acanthosomatidae (Heteroptera: Pentatomidae): keys to and descriptions of subfamilies, tribes and genera, with designation of types
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Perceptual restoration of obliterated sounds
Mutagenicity studies on two chromium(III) coordination compounds
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The joint commission: four key root causes loom large in sentinel event data
Treatment of vitiligo with topical 15% lactic acid solution in combination with ultra violet-A
Behaviour of dairy cows within three hours after feed supply: I. Influence of housing type and time elapsing after feed supply
Observations of the propagation velocity and formation mechanism of burst fractures caused by gunshot
Management and control of patients with type 2 diabetes mellitus in Lebanon: results from the International Diabetes Management Practices Study (IDMPS)
The diet composition and nutritional knowledge of patients with anorexia nervosa
Physoporella croatica Herak, 1958 of the Slovak karst Anisian (Slovakia, the West Carpathians Mts.)
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Duration of the life of plants in phylogeny

Muco lipidosis iv deficiency of ganglioside neuraminidase activity toward sialic acid galactose but not sialic acid sialic acid linkages


Muco lipidosis iv deficiency of ganglioside neuraminidase activity toward sialic acid galactose but not sialic acid sialic acid linkages



Pediatric Research 16(4 Part 2): 189A



ISSN/ISBN: 0031-3998


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(PDF emailed within 1 workday: $29.90)

Accession: 028752597

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Related references

Muco lipidosis i elevated level of sialic acid containing compounds and deficiency of a neuraminidase in cultured fibroblasts. Human Heredity 27(3): 168, 1977

The metabolic defect in muco lipidosis i accumulation of sialic acid containing compounds due to an alpha neuraminidase ec 3.2.1.18 deficiency. Hoppe-Seyler's Zeitschrift fuer Physiologische Chemie 358(10): 1189, 1977

Amino acid residues important for CMP-sialic acid recognition by the CMP-sialic acid transporter: analysis of the substrate specificity of UDP-galactose/CMP-sialic acid transporter chimeras. Glycobiology 22(12): 1731-1740, 2012

Incorporation of glycosidically linked sialic acid from radiolabeled free sialic acid and cytidine monophosphate-sialic acid by intact hamster fibroblasts: a reexamination. Biochemistry 19(9): 1893-1900, 1980

Content of gangliosides ano protein bound sialic acid in post mortem brain of patients with muco lipidosis i and muco lipidosis ii. Cellular and Molecular Biology 25(4): 281-284, 1979

Studies on sialic acid. III. Synthesis of sialic acid and a sialic acid-containing substance by Escherichia coli. Fukushima Jour Med Sci 6(1): 61-65, 1958

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Turnover of free sialic acid, CMP-sialic acid, and bound sialic acid in rat brain. Journal of Neurochemistry 36(4): 1492-1499, 1981

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Analysis of sialic acid-related substances and its clinical application. A. Analysis of sialic acid in clinical specimens other than sera. 1. Analysis of total urinary sialic acid, with special reference to the fluctuations in children. Rinsho Byori. Japanese Journal of Clinical Pathology Suppl. 54: 165-168, 1983

A sialic acid-like substance present in plants. Similarity of qunic acid to sialic acid in the 2-thiobarbituric acid reaction. Agricultural and Biological Chemistry 41(1): 215-216, 1977