Bronchopulmonary pathology in children with monogenic connective tissue diseases Marfans syndrome and Ehlers-Danlos syndrome
Shakhnazarova, M.D.; Rozinova, N.N.; Semyachkina, A.N.; Kostyuchenko, M.V.
Rossiiskii Vestnik Perinatologii i Pediatrii 52(3): 28-31
ISSN/ISBN: 1027-4065 Accession: 030362183
The paper considers different types of bronchopulmonary pathology in Marfan's syndrome and Ehlers-Danlos syndrome. It is shown that there are functional and X-ray signs of obstructive syndrome and emphysema in children even in the absence of clinical manifestations of lung diseases.