Section 41
Chapter 40,696

Micro-Ebstein. Presentation of 3 cases and analysis of the literature

Alitto, F.; Neri, G.; Mobilia, G.; Moro, E.

Minerva Cardioangiologica 38(12): 547-550


ISSN/ISBN: 0026-4725
PMID: 2092234
Accession: 040695795

The authors describe three cases of micro-Ebstein diagnosed using 2D-echocardiography in patients affected by extrasystolic cardiopalm. The most important echocardiographic criterion for diagnosis was an apical displacement of the septal cusp of the tricuspid valve of at least 8 mm/m2 BA. It is generally reported that the severity of arrhythmias is independent of the degree of tricuspid malformation. The anatomical substrates of arrhythmias are persistent anomalous muscular by-passes between the atrium and the ventricles, and intrinsic anomaly of the right ventricular myocardium. For these reasons, it is necessary to follow-up patients and monitor arrhythmias using Holter-ECG. Echocardiography is now recognised as being the most important tool for the identification of this anomaly.

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