+ Site Statistics
+ Search Articles
+ PDF Full Text Service
How our service works
Request PDF Full Text
+ Follow Us
Follow on Facebook
Follow on Twitter
Follow on LinkedIn
+ Subscribe to Site Feeds
Most Shared
PDF Full Text
+ Translate
+ Recently Requested

Acquired ciliary defects compared to those seen in the immotile-cilia syndrome



Acquired ciliary defects compared to those seen in the immotile-cilia syndrome



European Journal of Respiratory Diseases. Supplement 127: 5-10



An attempt is made to characterize injured cilia and ciliary mutants separately with particular emphasis on human conditions. The usefulness of electron microscopical investigations is stressed. An injury to a ciliated epithelium may very well be restricted to one site in the body and may appear at any stage of life. Typical ciliary mutants, such as are seen in the immotile-cilia syndrome, represent a generalized condition and will be found from the beginning of life. Some types of ciliary defects are relatively unspecific and found after various kinds of insult to the cilia also in the immotile-cilia syndrome; these are: compound cilia, supernumerary microtubules in the axoneme, and loss of cilia or of ciliated cells. Other kinds of ciliary defect seem to be typical of the ciliary mutants: absence of dynein arms, absence of spokes and central sheath, transposition of one of the central microtubules and short central microtubules.

Please choose payment method:






(PDF emailed within 1 workday: $29.90)

Accession: 042158023

Download citation: RISBibTeXText

PMID: 6578058


Related references

Cystic fibrosis compared with the immotile-cilia syndrome. A study of mucociliary clearance, ciliary ultrastructure, clinical picture and ventilatory function. Scandinavian Journal of Respiratory Diseases 59(6): 297-306, 1978

The dyskinetic cilia syndrome. Ciliary motility in immotile cilia syndrome. Chest 78(4): 580-582, 1980

Congenital defects in the ultrastructure of respiratory cilia in the immotile cilia syndrome. Clinical Research 26(6): 818A, 1978

The discovery of defects in respiratory cilia in the immotile cilia syndrome. Journal of Pediatrics 96(2): 244-247, 1980

Ciliary orientation in the immotile cilia syndrome. European Archives of Oto-Rhino-Laryngology 247(2): 100-103, 1990

Ciliary dyskinesis: the immotile cilia syndrome. Laryngoscope 93(5): 573-577, 1983

Ciliary abnormalities in immotile cilia syndrome. Journal of Cell Biology 95(2 Part 2): 321A, 1982

The immotile-cilia syndrome and other ciliary diseases. International Review of Experimental Pathology 19: 1-43, 1979

Heterogeneity of ciliary morphology in the immotile cilia syndrome in man. Journal of Ultrastructure Research 73(1): 34-43, 1980

Primary ciliary dyskinesia (the immotile cilia syndrome). Annals of Allergy 73(6): 457, 1994

Primary ciliary dyskinesia, immotile cilia syndrome, and Kartagener syndrome: diagnostic criteria. Schweizerische Medizinische Wochenschrift 126(11): 421-433, 1996

Immotile cilia syndrome and ciliary dyskinesia proposal of a diagnostic protocol. Rivista di Patologia e Clinica della Tubercolosi e di Pneumologia 59(1): 71-86, 1988

Immotile cilia syndrome and ciliary abnormalities induced by infection and injury. American Review Of Respiratory Disease: 107-109, 1981

Immotile cilia syndrome in three dogs from a litter Congenital ciliary dysfunction. Journal of the American Veterinary Medical Association5, 183(6): 667-672, 1983

Relative orientation of the ciliary central pair in the immotile cilia syndrome. Chest 91(2): 292, 1987