+ Site Statistics
+ Search Articles
+ PDF Full Text Service
How our service works
Request PDF Full Text
+ Follow Us
Follow on Facebook
Follow on Twitter
Follow on LinkedIn
+ Subscribe to Site Feeds
Most Shared
PDF Full Text
+ Translate
+ Recently Requested

Malignant systemic angioendotheliomatosis. Apropos of a case with an ultrastructural and histo-immunologic study

Malignant systemic angioendotheliomatosis. Apropos of a case with an ultrastructural and histo-immunologic study

Annales de Pathologie 4(1): 61-67

Clinico-pathological data in a typical case are compared with those of 54 published reports of systemic angioendotheliomatosis. In this rare disease the lesions, characterized by clusters of abnormal cells in the small vessels, usually have multivisceral localizations, with chiefly cutaneous and encephalic manifestations and a rapidly fatal course. However cases are known with lesions restricted to the skin and a protracted if not regressive course; about half of these cases are associated with an endocarditis. In the case reported, the results of ultrastructural and histo-immunological studies (f. VIII, lysozyme, anti-protease, Ig) are in favour of the endothelial origin of the abnormal cells, a now widely accepted hypothesis.

Please choose payment method:

(PDF emailed within 1 workday: $29.90)

Accession: 043579557

Download citation: RISBibTeXText

PMID: 6367764

Related references

Systemic malignant angio endotheliomatosis case report including ultrastructural and histo immunologic study. Annales de Pathologie 4(1): 61-68, 1984

Intravascular malignant lymphoma (malignant angioendotheliomatosis). Apropos of a case with histologic, immunohistochemical and ultrastructural studies. Archives d'Anatomie et de Cytologie Pathologiques 37(5-6): 208-212, 1989

Malignant angioendotheliomatosis Immunohistochemical, ultrastructural, and molecular genetics studies. Journal of Cutaneous Pathology 20(6): 562, 1993

Malignant hem angio peri cytoma ultrastructural and histo enzymological analysis of 1 case. Annales d'Anatomie Pathologique 23(1): 41-52, 1978

Neoplastic angioendotheliomatosis. A variant of malignant lymphoma immunohistochemical and ultrastructural observations of three cases. Ophthalmology 93(9): 1237-1245, 1986

Malignant angioendotheliomatosis mimicking systemic necrotizing vasculitis. Journal of Rheumatology 19(7): 1133-1135, 1992

Intravascular malignant lymphoma (proliferative systemic angioendotheliomatosis). Annales de Dermatologie et de Venereologie 115(11): 1221-1223, 1988

Malignant angioendotheliomatosis is an angiotropic intravascular lymphoma. Immunohistochemical, ultrastructural, and molecular genetics studies. American Journal of Dermatopathology 17(3): 242-248, 1995

Malignant intravascular lymphoma (malignant angioendotheliomatosis), with adrenal localization. Report of a case. Annales de Pathologie 12(2): 126-129, 1992

Angiotropic B-cell lymphoma (malignant angioendotheliomatosis): failure of systemic chemotherapy. British Journal of Dermatology 123(6): 807-810, 1990

Malignant hemangiopericytoma. Apropos of the ultrastructural and histoenzymological analysis of a case. Annales d'Anatomie Pathologique 23(1): 41-51, 1978

Apropos of a Case of "angioendotheliomatosis Proliferans Systematisata" (Tappeiner and Pfleger). Annales de Dermatologie et de Syphiligraphie 92: 129-138, 1965

Malignant angioendotheliomatosis--a true lymphoma: a case of intravascular malignant lymphomatosis studied by southern blot hybridization analysis. Human Pathology 19(4): 475-478, 1988

Intravascular malignant lymphomatosis (so-called malignant angioendotheliomatosis): a case confined to the lumbosacral spinal cord and nerve roots. Clinical Neuropathology 9(3): 115-120, 1990

Malignant angioendotheliomatosis: a clinical case. Revista Medica de Chile 116(9): 924-928, 1988