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Optic atrophy, sensorineural deafness and sensory neuropathy



Optic atrophy, sensorineural deafness and sensory neuropathy



Neurologia 9(2): 69-71



We present a patient with slowly progressing optic atrophy, sensorineural deafness and sensory neuropathy. Clinical examination and testing revealed the exclusively sensorineural nature of this syndrome. Nerve biopsy pointed to primary degeneration. Our review of the literature indicates that this syndrome is categorized as heredo-degenerative.

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Accession: 046870619

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PMID: 8204252


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