+ Site Statistics
+ Search Articles
+ PDF Full Text Service
How our service works
Request PDF Full Text
+ Follow Us
Follow on Facebook
Follow on Twitter
Follow on LinkedIn
+ Subscribe to Site Feeds
Most Shared
PDF Full Text
+ Translate
+ Recently Requested

Aortic root remodeling in a patient with Turner syndrome using the reference curves of aortic diameters in children



Aortic root remodeling in a patient with Turner syndrome using the reference curves of aortic diameters in children



General Thoracic and Cardiovascular Surgery 66(11): 667-670



We report the successful surgical treatment of aortic regurgitation in a 27-year-old woman with Turner syndrome (TS) who was admitted with exacerbation of dyspnea on exertion. Echocardiography showed a bicuspid aortic valve with severe aortic regurgitation and computed tomography showed dilatation of the ascending aorta and aortic root. Due to the patient's low body surface area (due to TS), standard determination of aortic size was not possible; therefore, we used the reference curves of aortic diameters in children. Because of the possibility of fatal ascending aortic dissection and rupture, we performed concomitant aortic root remodeling and aortic valve repair.

Please choose payment method:






(PDF emailed within 0-6 h: $19.90)

Accession: 048585584

Download citation: RISBibTeXText

PMID: 29372397

DOI: 10.1007/s11748-018-0889-y


Related references

Screening for aortic root dilation in marfan syndrome using the ratio of the aortic root to descending aortic diameters in children. Journal of the American Society of Echocardiography 22(10): 1109-1113, 2009

Aortic dilatation resulting in chronic aortic regurgitation and complicated by aortic dissection in a patient with Turner's syndrome. Clinical Cardiology 7(4): 233-235, 1984

Moderate aortic enlargement and bicuspid aortic valve are associated with aortic dissection in Turner syndrome: report of the international turner syndrome aortic dissection registry. Circulation 126(18): 2220-2226, 2012

Valve-sparing aortic root replacement and remodeling with complex aortic valve reconstruction in children and young adults with moderate or severe aortic regurgitation. Journal of Thoracic and Cardiovascular Surgery 147(6): 1768-1774, 2014

Unicuspid aortic valve and aortic arch aneurysm in a patient with Turner syndrome. Asian Cardiovascular and Thoracic Annals 16(3): 266-267, 2008

Aortic root morphology in patients undergoing percutaneous aortic valve replacement: evidence of aortic root remodeling. Journal of Thoracic and Cardiovascular Surgery 137(4): 950-956, 2009

Acute aortic dissection, aortic insufficiency, and a single coronary artery in a patient with Turner's syndrome. Journal of Cardiovascular Surgery 36(3): 273-275, 1995

Aortic root remodeling and external aortic annuloplasty to treat sinus of Valsalva aneurysm in a patient with complete situs inversus. Journal of Cardiothoracic Surgery 10: 182, 2015

Aortic root motion remodeling after aortic valve replacement--implications for late aortic dissection. Interactive Cardiovascular and Thoracic Surgery 7(3): 407, 2008

Perioperative dynamic morphological changes of the aortic annulus during aortic root remodeling with aortic annuloplasty at systolic and diastolic phases. Journal of Heart Valve Disease 17(4): 366-370, 2008

A case of combined operation of aortic valve slicing and root remodeling for ascending aortic aneurysm with aortic regurgitation. Kyobu Geka. Japanese Journal of Thoracic Surgery 54(7): 589-592, 2001

Aortic root conservative repair of acute type A aortic dissection involving the aortic root: fate of the aortic root and aortic valve function. Journal of Thoracic and Cardiovascular Surgery 146(5): 1113-1118, 2013

Dynamic normal aortic root diameters: implications for aortic root reconstruction. Annals of Thoracic Surgery 91(2): 485-489, 2011

Determinants of Increased Aortic Diameters in Young Normotensive Patients With Turner Syndrome Without Structural Heart Disease. Pediatric Cardiology 39(4): 786-793, 2018

Evaluation of left ventricular reverse remodeling in patients with severe aortic regurgitation undergoing aortic valve replacement: Comparison between diameters and volumes. Echocardiography 35(2): 142-147, 2018