+ Site Statistics
+ Search Articles
+ PDF Full Text Service
How our service works
Request PDF Full Text
+ Follow Us
Follow on Facebook
Follow on Twitter
Follow on LinkedIn
+ Subscribe to Site Feeds
Most Shared
PDF Full Text
+ Translate
+ Recently Requested

Complex sleep apnea syndrome in a child with Chiari malformation type 1



Complex sleep apnea syndrome in a child with Chiari malformation type 1



Turkish Journal of Pediatrics 55(1): 107-111



There are few reports of a patient presenting with symptoms of obstructive sleep apnea syndrome (OSAS) as the sole manifestation of Chiari malformation type 1 (CM1). In the literature, complex sleep apnea syndrome (CompSAS) was also reported as a rare condition related to CM1 patients. We report the case of a 13-year-old patient with the complaint of snoring and difficulty in breathing during sleep, but otherwise healthy. After an initial polysomnography, the patient was diagnosed with OSAS and nocturnal continuous hypoxemia. The child underwent titration to pressure of continuous positive airway pressure (CPAP); obstructive apnea improved but central apnea (i.e., CompSAS) and nocturnal continuous hypoxemia persisted. Magnetic resonance imaging led to diagnosis of CM1. Her central apnea and nocturnal hypoxemia resolved following bi-level positive airway pressure-spontaneous-timed (S/T) (BiPAPS/ T) treatment. We emphasize that the CM1 cases can admit with only breathing problems during sleep without concomitant neurological findings, and this malformation can cause central apnea resistant to CPAP.

Please choose payment method:






(PDF emailed within 1 workday: $29.90)

Accession: 052262837

Download citation: RISBibTeXText

PMID: 23692844


Related references

Chiari 1 Malformation in a Child with Febrile Seizures, Parasomnias, and Sleep Apnea Syndrome. Case Reports in Pediatrics 2017: 8189790, 2017

Sleep apnea syndrome associated with a type I Chiari malformation. Brain and Development 24(1): 49-51, 2002

Sleep apnea syndrome associated with a type I Chiari malformation. Brain & Development 24(1): 49-51, 2002

Sleep apnea-hypopnea syndrome in type 1 Chiari malformation. Anales de Pediatria 79(4): 273-274, 2013

Central sleep apnea syndrome as the first sign of type I Chiari malformation. Anales de Pediatria 68(3): 277-281, 2008

Respiratory failure and sleep apnea in arnold chiari type ii malformation and a trial to prevent sleep apnea with transcutaneous electrical stimulation. Journal of Neurology 232(Suppl.): 161, 1985

Syringomyelia and Chiari type 1 malformation with associated bilateral vocal cord paralysis and obstructive sleep apnea syndrome. Revista Espanola de Anestesiologia Y Reanimacion 52(10): 639-641, 2005

Obstructive sleep apnea-hypopnea syndrome associated with type II Arnold-Chiari malformation. Benefits of neurosurgical intervention. Anales de Pediatria 78(3): 195-198, 2013

Type I Chiari malformation presenting central sleep apnea. Auris Nasus Larynx 41(2): 222-224, 2014

Isolated sleep apnea due to Chiari type I malformation and syringomyelia. Pediatric Neurology 13(3): 266-267, 1995

Arnold-Chiari malformation presenting as sleep apnea syndrome. Sleep Medicine 1(2): 139-144, 2000

A sudden-death in a case of Arnold-Chiari malformation (type I) with sleep apnea. No to Shinkei 37(6): 575-581, 1985

Sleep apnea and vocal cord paralysis secondary to type I Chiari malformation. Pediatrics 80(2): 231-234, 1987

A sudden death case of arnold chiari malformation type i with sleep apnea. Brain & Nerve 37(4): 575-581, 1985

Surgical History of Sleep Apnea in Pediatric Patients with Chiari Type 1 Malformation. Neurosurgery Clinics of North America 26(4): 543-553, 2015