Section 59
Chapter 58,151

Intraspinal extradural benign fibrous histiocytoma of the lumbar spine in a pediatric patient. Case report and literature review

Donati, F.; Proietti, L.; Burrofato, A.; Santagada, D.Alessandro.; Tamburrelli, F.Ciro.

Child's Nervous System: Chns: Official Journal of the International Society for Pediatric Neurosurgery 32(8): 1549-1553


ISSN/ISBN: 0256-7040
PMID: 26984808
DOI: 10.1007/s00381-016-3056-8
Accession: 058150790

Benign fibrous histiocytoma (BFH) is a rare skeletal tumor. Spinal localizations have been previously described in 17 cases, and this is the first report of BFH occurring at the lumbar spine in a pediatric patient. A 13-year-old male complained lower limb motor and sensory impairment with severe claudication and urination disorders. A huge intraspinal, extradural mass at L4-L5 level, clearly evident on a preoperative MRI, caused dislocation and severe compression of the cauda equina nerve roots. After a biopsy, confirming BFH, a tumor resection and L4-S1 vertebral arthrodesis was carried out. At 1 year follow-up, no recurrence was detached on postoperative MRI, with complete neurological recovery. Review of the literature is discussed. Histological examination is mandatory for a correct diagnosis and plan of treatment. None of the pediatric patients treated for BFH have ever shown local relapse.

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